Abstract:
The invention relates, in part, to improved methods of administering α-galactosidase A for the treatment of α-galactosidase A deficiencies including Fabry disease.
Abstract:
A system creates a desired current level within a traffic signal. A power supply unit receives an external power signal and transforms the power signal to a lamp current. A pulse generator monitors the value of the lamp current and automatically adjust the power usage of the current sink circuit to maintained a predefined current amplitude. A current pulser generates square current pulses at a frequency based at least in part on the frequency of the lamp current. A current sink superimposes the rectangular current pulse onto the lamp current and outputs a combined power signal to the alternating current power line.
Abstract:
A tubular fluid flow device of varying outside dimensions adapted for use in a high pressure, rapidly cycling temperature environment, an isolation ball valve, a ball valve isolation method and a catalyst transfer method. The flow device 10 can have a tubular member 12 having at least one locus 14, 16 of non-uniform outside dimension and an axial flow passage 20 with a uniform inside diameter between opposite end connection elements. A thermal sleeve liner 22 can be disposed about the axial flow passage in a bore 24 formed in the tubular member, wherein the sleeve comprises an outer surface having a thermal barrier coating 26. A pressure-relief passage 28 is provided in fluid communication between the axial flow passage and an interface between an exterior surface of the thermal sleeve liner and an inner surface of the bore.
Abstract:
A tubular fluid flow device of varying outside dimensions adapted for use in a high pressure, rapidly cycling temperature environment, an isolation ball valve, a ball valve isolation method and a catalyst transfer method. The flow device 10 can have a tubular member 12 having at least one locus 14, 16 of non-uniform outside dimension and an axial flow passage 20 with a uniform inside diameter between opposite end connection elements. A thermal sleeve liner 22 can be disposed about the axial flow passage in a bore 24 formed in the tubular member, wherein the sleeve comprises an outer surface having a thermal barrier coating 26. A pressure-relief passage 28 is provided in fluid communication between the axial flow passage and an interface between an exterior surface of the thermal sleeve liner and an inner surface of the bore.
Abstract:
A test cell and method for stress testing a test specimen including a first platen and a second platen. Each platen having a loading surface, an inclined surface, and a longitudinal axis. The inclined surface being inclined relative to the longitudinal axis at an angle and the inclined surface having a specimen recess formed therein for receiving a portion of the test specimen such that when the inclined surface of the second platen is positioned in a face-to-face relationship with the inclined surface of the first platen, a shear stress is applied to the test specimen when an axial load is applied to the first and second platens. The platens further including fluid ports to subject the test specimen to fluid flow at various pressures and fluid chemistries and ultrasonic transducers to determine acoustic, compressional, and shear wave velocities and in multiple orientations.
Abstract:
A photonic integrated circuit (PIC) chip comprising an array of modulated sources, each providing a modulated signal output at a channel wavelength different from the channel wavelength of other modulated sources and a wavelength selective combiner having an input optically coupled to received all the signal outputs from the modulated sources and provide a combined output signal on an output waveguide from the chip. The modulated sources, combiner and output waveguide are all integrated on the same chip.
Abstract:
A wafer probe head assembly for providing signal paths between an integrated circuit (IC) tester and input/output, power and ground pads on the surfaces of ICs formed on a wafer to be tested includes inter alia, an adapter board and a probe card assembly including a space transformer and a contactor carrying substrate having a substantially planar bottom surface with printed or plated circuit traces formed thereon and a plurality of contactors plated to or photo-lithographically formed on the traces and arranged to simultaneously ohmically engage the contact pads of one or more ICs on a wafer under test. The contactors may include resilient supporting structures attached to or integrated with the signal carrying circuit traces. The probe card assembly may also include one or more substrate layers with the circuit traces and vias formed on and/or within the substrate layers to facilitate connection of the tester signal carrying conductors to the contactors.
Abstract:
An electric compound aircraft is disclosed with a capability of making vertical takeoff and landing and forward flight. In a specific embodiment, the compound aircraft includes an electric motor-powered tip-jet-driven rotary wing, an electric motor-powered tip-jet-driven propeller. The rotary wing provides lift for vertical takeoff and landing, hovering capability and during flight. The propeller provides thrust for forward flight. A fixed wing can be used, in addition to the rotary wing to provide lift for forward flight. Various electric control devices are used to provide control and stability for the compound aircraft and automation.
Abstract:
The invention relates, in part, to improved methods of administering α-galactosidase A for the treatment of α-galactosidase A deficiencies including Fabry disease.
Abstract:
A nanoporous polymer electrolyte and methods for making the polymer electrolyte are disclosed. The polymer electrolyte comprises a crosslinked self-assembly of a polymerizable salt surfactant, wherein the crosslinked self-assembly includes nanopores and wherein the crosslinked self-assembly has a conductivity of at least 1.0×10−6 S/cm at 25° C. The method of making a polymer electrolyte comprises providing a polymerizable salt surfactant. The method further comprises crosslinking the polymerizable salt surfactant to form a nanoporous polymer electrolyte.
Abstract translation:公开了纳米多孔聚合物电解质和制备聚合物电解质的方法。 聚合物电解质包括可聚合盐表面活性剂的交联自组装体,其中所述交联的自组装体包括纳米孔,并且其中所述交联的自组装体的导电率至少为1.0×10 -6 / cm 3 在25℃下制备聚合物电解质的方法包括提供可聚合盐表面活性剂。 该方法还包括交联可聚合盐表面活性剂以形成纳米多孔聚合物电解质。